TY - JOUR
T1 - Hereditary lymphedema of the leg – A Case Report
AU - Heinig, Birgit
AU - Lotti, Torello
AU - Tchernev, Georgi
AU - Wollina, Uwe
PY - 2017
Y1 - 2017
N2 - Primary of hereditary lymphedema is a rare but progressive disease. It is yet not curable. We present a 48-year-old male patient with hereditary lymphedema of his left leg, that was realised by minor trauma (able twist) when he was seven years old. He had never been treated for lymphedema but experienced multiple erysipelas during his life. After diagnostic procedures to exclude other causes of leg swelling, the diagnosis of hereditary lymphedema of the leg, stage III was confirmed. We initialized complex decongestive therapy. During two weeks of intensive treatment, the circumference of the left leg could be reduced by 10 cm. This case illustrates the "natural course" hereditary lymphedema. But it raises the hope that even after decades of ignorance, the patients benefits from complex decongestive treatment. Therapeutic nihilism is unnecessary and poses lymphedema patients to risks of infection and secondary malignancies like Stewart-Trewes syndrome.
AB - Primary of hereditary lymphedema is a rare but progressive disease. It is yet not curable. We present a 48-year-old male patient with hereditary lymphedema of his left leg, that was realised by minor trauma (able twist) when he was seven years old. He had never been treated for lymphedema but experienced multiple erysipelas during his life. After diagnostic procedures to exclude other causes of leg swelling, the diagnosis of hereditary lymphedema of the leg, stage III was confirmed. We initialized complex decongestive therapy. During two weeks of intensive treatment, the circumference of the left leg could be reduced by 10 cm. This case illustrates the "natural course" hereditary lymphedema. But it raises the hope that even after decades of ignorance, the patients benefits from complex decongestive treatment. Therapeutic nihilism is unnecessary and poses lymphedema patients to risks of infection and secondary malignancies like Stewart-Trewes syndrome.
KW - Complex decongestive therapy
KW - Elephantiasis nostra
KW - Erysipelas
KW - Fibrosis
KW - Immunocompromised district
KW - Primary lymphedema
KW - Secondary lymphedema
UR - http://resolver.tudelft.nl/uuid:b4e83364-88c1-4ed0-845d-847f4ceea127
UR - http://www.scopus.com/inward/record.url?scp=85027402446&partnerID=8YFLogxK
U2 - 10.3889/oamjms.2017.082
DO - 10.3889/oamjms.2017.082
M3 - Article
AN - SCOPUS:85027402446
SN - 1857-9655
VL - 5
SP - 451
EP - 453
JO - Open Access Macedonian Journal of Medical Sciences
JF - Open Access Macedonian Journal of Medical Sciences
IS - 4 Special Issue GlobalDermatology
ER -